Download Citation on ResearchGate | DERMATOMIOSITIS JUVENIL Y EMBARAZO | The juvenile dermatomyositis is a chronic inflammatory. Palabras clave: Dermatomiositis, debilidad muscular, miopatía. La dermatomiositis (DM) es una enfermedad que, junto . Tipo IV. Dermatomiositis juvenil. Summary. Epidemiology. The exact prevalence of JDM is not known. Estimated annual incidence rates range from 1/, to 1/, Females are affected .
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Treatment is generally dermatomiossitis, with very low mortality rates reported. New England Journal of Medicine. Clinical significance of specific autoantibodies in juvenile dermatomyositis. Reported malignancies include lymphoma and leukemia. About half of children with JDMS also have pain in their muscles. Specialised Social Services Eurordis directory.
The Impact Factor measures the average number of citations received in a particular year by papers published in the juveil during the two receding years. Eur J Med1 1: Generalized edema as a form of presentation of juvenile dermatomyositis. Arch Dermatol,pp.
Las enfermedades incluidas en este grupo son:. Value of nuclear magnetic resonance in juvenile dermatomyositis. La globulina inmune intravenosa es cara y se necesitan repetidas dosis.
Pathophysiology and disease expression.
Patients commonly have the signs of DM, i. Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. MR findings in this disease may be useful in establishing its diagnosis within the clinical context. SJR uses a similar algorithm as the Google page rank; it provides a quantitative and qualitative measure of the journal’s impact. Cutaneouschanges of dermatomyositis precede muscle weakness.
Systemic connective tissue disorders M32—M36 J Rheumatol, 13pp. Juvenile dermatomyositis suspicious should be made upon muscle weakness and general symptoms. A palabras de los doctores, este hecho pudo ser un indicador, que por desgracia para todos pasaba desapercibido. Conclusions The results of our review agree with other series reported.
The underlying cause of JDM is unknown. Arthritis Rheum, 35pp. The aim of treatment is to reduce long-term morbidity and to restore physical function. Show all Show less. Views Read Edit View history.
Dermatomiositis en la infancia | Anales de Pediatría
The JDMS rash usually occurs as the initial symptom. Proximal muscle weakness, characteristic skin rash and elevated muscle enzymes are routinely used to identify JDM. J Dermatol, 19pp. It is thought to be related to complement-mediated changes in small vessels in muscle tissue leading to vascular damage. Physical therapy is important to maintain or restore muscle strength. Se recomienda comenzar precozmente el tratamiento con corticoides. Juvenile dermatomyositis JDM is an idiopathic inflammatory myopathy IMM of presumed autoimmune dysfunction resulting in muscle weakness among other complications.
Other signs may include falling, dysphoniaor dysphagia.
J Rheumatol, 22pp. SNIP measures contextual citation impact by wighting citations based on the total number of citations in a subject field. Bohan Am, Peter JB. J Urol,pp.
Subscribe to our Newsletter. The muscles first affected tend to be proximal i. Check this box if you wish to receive a copy of your message. Hospital 12 de Octubre. Treatment with steroids should be started promptly.
Macrophage activation syndrome, a severe sometimes life-threatening condition, has been described in some children diagnosed dermatomoositis JDM.
Risk of cancer in patients with dermatomyositis or polymyositis. Other associated extramuscular features include dysphagia, sometimes dysphonia, hoarseness, pneumonitis, cardiac manifestations dermatojiositis defects, myocarditis, dilated cardiomyopathy, see this term. Aggressive therapy for childhood rheumatic diseases. Once the oral steroids are reduced to a less toxic level, the sparing agents can also be gradually withdrawn.
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