PDF | The majority of oral diseases present as growths and masses of varied cellular origin. Such masses may include simple hyperplasia. The presence of a neurovascular hamartoma within the oral cavity is truly a rare entity. Scarcely reported in the literature, these hamartomas. Cowden’s Syndrome, Bannayan-Riley-Ruvalcaba Syndrome, PTEN Hamartoma Tumour Syndrome.

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Hamartomas of the oral cavity.

A lesion searching for a name. Histologically, they show presence of mature neural and striated muscle tissue.

Clinical, radiographic features and management options. In view of the high lifetime risk of malignancy it is important to keep patients under close surveillance.

The majority of oral diseases present as growths and masses of varied cellular origin. Microscopically, the proliferative phase of IH and CH comprises complex cellular mixtures, chiefly the endothelial cells. Thus resulting in lesser aggressive biological behavior and increased cytodifferentiation and apoptosis in AOT than ameloblastomas [35,36]. Rhabdomyomatous mesenchymal hamartoma presenting as haemangioma on the upper lip: Suzuki H, Hashimoto K. Hamartomatous Growth of Mesenchymal Derivatives.

OGCF was described by Philipsen et al [8]the histopathology of the tissue shows no caviry with dense fibrous connective tissue containing large multinucleated giant cells, proliferating odontogenic islands with cavityy squamous metaplasia. J Oral Maxillofac Pathol.

Hamartomas of the oral cavity Patil S, Rao RS, Majumdar B – J Int Soc Prevent Communit Dent

Suzuki H, Hashimoto K. Prevalence of enamel pearls in teeth from a human teeth bank. Oral-facial-digital syndrome type 1. Vascular malformation VM refers to congenital morphogenic anomalies of the various vessels.


Congenital granular cell tumour is thought to be a variant of granular cell tumour, but the exact nature of the lesion is unclear. This group of lesion is frequently associated with the dental follicle and hence has a close link to the dental follicle hamartomas.

Hamartomas are frequently encountered in major organs like liver, lung, pancreas etc. Histopathologically it shows clusters of odontogenic epithelial which are bordered by a fibrous pseudocapsule. How do I follow my topics’ performance?

Clinically, it occurs in multiple small masses.

Benign fibro-osseous lesions of the craniofacial complex. Current management of hemangiomas and vascular malformations. Figure 3 Ameloblastic fibroodontoma. The pathobiology of these lesions is sometimes understated.

Hamartomas of the oral cavity

There have been reported cases of root resorption associated with AOT [32]. Immunohistological features in adenomatoid odontogenic tumor: This is almost never in the case of neoplasm, where the neoplastic cells are clonally derived.

They represent deposits of enamel located at the cemento-enamel junction or at the furcation area. Marx RE, Stern D. A Rationale for Diagnosis and Treatment; pp.

Proteus syndrome is a rare congenital hamartomatous condition with an incidence of less than 1 in a population of 1 million. Given the non-neoplastic nature of hamartomas, conservative surgical excision is the treatment of choice. Neurofibroma As the name indicates, it is an admixture of perineural fibroblasts and Schwann cells. Author information Copyright and License information Disclaimer. Benign fibro-osseous lesions of the craniofacial complex. Leiomyomatous hamartoma Leiomyomatous hamartoma is another rare entity which commonly involves the midline of palate and tongue.


Hamartomas, which are dysmorphic or morphologically altered proliferation of cells native to the organ in which they arise, gain a certain size before ceasing their proliferation. Nevertheless, not all the lesions stated as hamartomas in the literature justify completely the above features.

Hamartomas of the oral cavity

Quintessence Publishing Co, Inc; Rhabdomyomatous mesenchymal hamartoma presenting as haemangioma on the upper lip: It commonly involves permanent first and second molars. Numerous cords of odontogenic epithelium and attempts of hard tissue formation.

This article has been cited by. According to the data tabulated in Table 1the most important features perceived are its limited hamartoma potential after adolescence, microscopic appearance of unencapsulated admixture of mature cells native to the anatomic location and association with chromosomal aberrations. Ameloblastic fibroma also included in the category of mixed odontogenic lesions.

Benign triton tumor of the trigeminal nerve.